ICD-10 Code E03.1 – Congenital hypothyroidism without goiter (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code E03.1 – Congenital hypothyroidism without goiter
What it is
This code identifies hypothyroidism present at birth without thyroid enlargement. It means the thyroid gland does not produce enough hormone, and no goiter is documented.
Clinical signs
Clinical features vary; refer to documentation. Commonly recorded findings include poor feeding, prolonged jaundice, constipation, lethargy, and delayed growth or development.
When to use this code
Use E03.1 when the provider documents congenital hypothyroidism and specifically notes no goiter. It is appropriate for newborn, infant, or pediatric records where the condition is confirmed or carried forward as an established diagnosis. If the chart does not state whether goiter is present, check documentation.
Do not use for
Do not use this code for acquired hypothyroidism or for congenital hypothyroidism with goiter. If the thyroid enlargement is documented, use the code that matches that finding.
Coding tip
Verify that “congenital” and “without goiter” are both documented before assigning E03.1.