ICD-10 Code E00.9 – Congenital iodine-deficiency syndrome, unspecified (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code E00.9 – Congenital iodine-deficiency syndrome, unspecified
What it is
E00.9 identifies congenital iodine-deficiency syndrome when the specific manifestation is not documented. It is used for a congenital condition caused by iodine deficiency, with the exact subtype left unspecified.
Clinical signs
Clinical features vary; refer to documentation. Standard references describe findings such as growth delay, developmental impairment, and other congenital abnormalities associated with iodine deficiency.
When to use this code
Use E00.9 when the record states congenital iodine-deficiency syndrome but does not specify the exact form or severity. It also fits when the clinician documents a congenital iodine-deficiency condition without further detail. If the chart names a more specific subtype, code that instead.
Do not use for
Do not use this code for acquired hypothyroidism, nonspecific iodine deficiency without congenital syndrome, or a clearly documented more specific congenital iodine-deficiency diagnosis. Check documentation.
Coding tip
Query for the exact congenital subtype whenever the note only says “iodine deficiency” or “congenital syndrome” without detail.