ICD-10 Code D64.0 – Hereditary sideroblastic anemia (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code D64.0 – Hereditary sideroblastic anemia
What it is
D64.0 identifies an inherited form of sideroblastic anemia, a disorder in which the body cannot properly incorporate iron into red blood cells. You use it when documentation confirms a hereditary cause rather than an acquired one.
Clinical signs
Clinical features vary; refer to documentation. Common references describe anemia with evidence of iron accumulation in marrow and ring sideroblasts, often confirmed by hematology evaluation or genetic findings.
When to use this code
Use D64.0 when the provider documents hereditary sideroblastic anemia, familial sideroblastic anemia, or a clearly inherited sideroblastic disorder. It may also apply when the record links the anemia to a known inherited syndrome. If the cause is not specified, check documentation before assigning this code.
Do not use for
Do not use this code for acquired sideroblastic anemia, anemia of chronic disease, or other unspecified anemias. If the chart does not state a hereditary cause, do not assume D64.0.
Coding tip
Look for wording such as “hereditary,” “familial,” or a documented genetic diagnosis before coding D64.0.