ICD-10 Code D47.01 – Cutaneous Mastocytosis (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code D47.01 – Cutaneous mastocytosis
What it is
D47.01 identifies cutaneous mastocytosis, a disorder in which mast cells accumulate in the skin. Use it when documentation specifically describes a skin-limited mast cell condition.
Clinical signs
Findings may include brownish or red-brown skin lesions, itching, flushing, or whealing after rubbing. Clinical features vary; refer to documentation.
When to use this code
Use D47.01 when the provider documents cutaneous mastocytosis, mastocytoma, or another skin-only mast cell disorder. It is appropriate when the record supports a dermatologic diagnosis without clear systemic involvement. If the note is vague, check documentation before coding.
Do not use for
Do not use this code for systemic mastocytosis or for nonspecific rash, urticaria, or pruritus without a documented mast cell disorder. Check documentation.
Coding tip
Code D47.01 only when the chart clearly states cutaneous mastocytosis; otherwise, query for the exact diagnosis.