ICD-10 Code E70.0 – Classical phenylketonuria (2026): Diagnosis, Symptoms & Billing Guide
The ICD-10 code for Classical phenylketonuria is E70.0.2026 ICD-10-CM Diagnosis Code E70.0 – Classical phenylketonuria Related ICD-10 Codes Parent code: E70 – Disorders of aromatic amino-acid metabolism Other codes in same category: E70.1 – Other hyperphenylalaninemias, E70.2 – Disorders of tyrosine metabolism, E70.20 – Disorder of tyrosine metabolism, unspecified, E70.21 – Tyrosinemia, E70.29 – Other…