ICD-10 Code G71.036 – Limb girdle muscular dystrophy due to fukutin related protein dysfunction (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code G71.036 – Limb girdle muscular dystrophy due to fukutin related protein dysfunction
What it is
This code identifies a hereditary muscular dystrophy affecting the shoulder and hip girdle muscles. It is used when the weakness is specifically linked to fukutin-related protein dysfunction.
Clinical signs
Typical findings include progressive proximal muscle weakness, difficulty rising, climbing stairs, or lifting the arms. Clinical features vary; refer to documentation for genetic or neuromuscular confirmation.
When to use this code
Use this code when the provider documents limb girdle muscular dystrophy caused by fukutin-related protein dysfunction. It may also apply when the diagnosis is confirmed by genetics, biopsy, or neuromuscular evaluation and the record names this subtype.
Do not assign a nonspecific muscular dystrophy code if the subtype is clearly documented. Check documentation if the record only states limb girdle muscular dystrophy without the causative protein defect.
Do not use for
Do not use it for other limb girdle muscular dystrophy subtypes or for unspecified muscular dystrophy. If the note does not identify fukutin-related protein dysfunction, check documentation.
Coding tip
Capture the exact genetic subtype from the assessment or test result before coding, because the specific cause determines this code.