ICD-10 Code G71.033 – Limb girdle muscular dystrophy due to dysferlin dysfunction (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code G71.033 – Limb girdle muscular dystrophy due to dysferlin dysfunction
What it is
Use this code for limb-girdle muscular dystrophy caused by dysferlin dysfunction, a genetic muscle disease that mainly weakens the hip and shoulder muscles. It reflects a specific subtype, not a general muscular dystrophy diagnosis.
Clinical signs
Typical findings include progressive proximal muscle weakness, difficulty climbing stairs, rising from a chair, or lifting the arms. Clinical features vary; refer to documentation, and confirm the dysferlin-related diagnosis when recorded.
When to use this code
Assign G71.033 when the provider documents limb-girdle muscular dystrophy due to dysferlin dysfunction, dysferlinopathy, or a clearly equivalent diagnosis. Use it for confirmed encounters, problem lists, or assessments that identify this specific genetic subtype. If the chart only says muscular dystrophy, check documentation before coding.
Do not use for
Do not use this code for unspecified muscular dystrophy, other limb-girdle muscular dystrophy types, or weakness without a documented dystrophy diagnosis. Check documentation if the record does not clearly link the condition to dysferlin dysfunction.
Coding tip
Code the specific subtype only when the provider names dysferlin dysfunction; otherwise, query or code the documented unspecified condition.