ICD-10 Code G71.032 – Autosomal recessive limb girdle muscular dystrophy due to calpain-3 dysfunction (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code G71.032 – Autosomal recessive limb girdle muscular dystrophy due to calpain-3 dysfunction
What it is
This code identifies an inherited muscular dystrophy that weakens the pelvic and shoulder girdle muscles. It is specifically linked to calpain-3 dysfunction and follows an autosomal recessive pattern.
Clinical signs
Typical findings include progressive proximal muscle weakness, difficulty rising from a chair, climbing stairs, or lifting the arms. Clinical features vary; refer to documentation.
When to use this code
Use this code when the provider documents autosomal recessive limb girdle muscular dystrophy caused by calpain-3 dysfunction, also known in some records as calpainopathy. Code it when the diagnosis is confirmed or clearly stated in the assessment.
Do not assign it for nonspecific myopathy or for limb girdle muscular dystrophy without a documented calpain-3 cause. Check documentation if the subtype is not explicit.
Do not use for
Do not use this code for other muscular dystrophies, acquired muscle weakness, or unspecified limb girdle muscular dystrophy. If the record does not name calpain-3 dysfunction, use the more specific documented diagnosis or check documentation.
Coding tip
Look for the exact genetic subtype in the chart; the code depends on documented calpain-3 involvement, not just the limb girdle muscular dystrophy label.