ICD-10 Code G71.031 – Autosomal dominant limb girdle muscular dystrophy (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code G71.031 – Autosomal dominant limb girdle muscular dystrophy
What it is
This code identifies an inherited muscular dystrophy that mainly affects the shoulder and pelvic girdle muscles. It is used when documentation specifies an autosomal dominant form of limb-girdle muscular dystrophy.
Clinical signs
Patients typically have progressive proximal muscle weakness, such as difficulty climbing stairs, rising from a chair, or lifting objects. Clinical features vary; refer to documentation for the specific subtype and confirmed findings.
When to use this code
Use this code when the provider documents autosomal dominant limb-girdle muscular dystrophy or an equivalent confirmed diagnosis. It also fits genetic or neuromuscular assessments that clearly identify this inheritance pattern. If the record only says “muscular dystrophy,” check documentation before coding.
Do not use for
Do not use this code for unspecified muscular dystrophy, other inherited myopathies, or acquired muscle weakness. Check documentation if the chart does not clearly state an autosomal dominant limb-girdle muscular dystrophy diagnosis.
Coding tip
Code the documented subtype and inheritance pattern exactly as recorded; if either is missing, query the provider.