ICD-10 Code G40.C19 – Lafora progressive myoclonus epilepsy, intractable, without status epilepticus (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code G40.C19 – Lafora progressive myoclonus epilepsy, intractable, without status epilepticus
What it is
This code identifies Lafora progressive myoclonus epilepsy that is documented as intractable and not currently in status epilepticus. It reflects a severe, progressive epilepsy syndrome with persistent seizure control problems.
Clinical signs
Typical findings include myoclonic jerks, generalized seizures, and progressive neurologic decline. Clinical features vary; refer to documentation for confirmed Lafora disease and seizure refractoriness.
When to use this code
Use this code when the record specifically states Lafora progressive myoclonus epilepsy and indicates the seizures are intractable. You should also confirm that status epilepticus is not present. If the note only says myoclonus epilepsy or progressive epilepsy, check documentation before assigning G40.C19.
Do not use for
Do not use it for epilepsy without documentation of Lafora disease or without intractability. Do not use it when status epilepticus is documented instead; select the appropriate code for that condition.
Coding tip
Verify both “intractable” and “without status epilepticus” in the provider note before coding.