ICD-10 Code G40.B11 – Juvenile myoclonic epilepsy, intractable, with status epilepticus (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code G40.B11 – Juvenile myoclonic epilepsy, intractable, with status epilepticus
What it is
This code identifies juvenile myoclonic epilepsy that does not respond well to treatment and is documented with status epilepticus. Use it when the record clearly supports both the epilepsy subtype and the ongoing seizure emergency.
Clinical signs
Typical documentation includes recurrent myoclonic jerks, often with generalized seizures, in a patient diagnosed with juvenile myoclonic epilepsy. Status epilepticus means seizures are prolonged or recur without recovery; clinical features vary, refer to documentation.
When to use this code
Use this code when the provider documents juvenile myoclonic epilepsy as intractable and also states status epilepticus. It is appropriate for encounters focused on seizure escalation, emergency evaluation, or continued management of a known refractory epilepsy syndrome. If the record does not clearly confirm both elements, check documentation.
Do not use for
Do not use this code for juvenile myoclonic epilepsy without intractability or without status epilepticus. Do not assign it when the seizure type or epilepsy syndrome is unspecified or better supported by another code.
Coding tip
Code only when the note explicitly links juvenile myoclonic epilepsy, intractable disease, and status epilepticus.