ICD-10 Code G40.834 – Dravet syndrome, intractable, without status epilepticus (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code G40.834 – Dravet syndrome, intractable, without status epilepticus
What it is
This code identifies Dravet syndrome, a severe epilepsy syndrome that remains difficult to control with treatment, without current status epilepticus. Use it when the diagnosis is documented and the seizures are described as intractable.
Clinical signs
Typical features include recurrent seizures beginning in early childhood, often with developmental delay and multiple seizure types. Clinical features vary; refer to documentation.
When to use this code
Use this code when the record specifically documents Dravet syndrome and notes that the seizures are intractable. It also applies when the provider states the patient has Dravet syndrome without status epilepticus at the time of the encounter. If the chart does not confirm intractability or the syndrome type, check documentation.
Do not use for
Do not use this code for Dravet syndrome with status epilepticus, or when seizure control is not documented as intractable. Do not use it for other epilepsy syndromes or nonspecific seizure disorders.
Coding tip
Match the code to the provider’s exact wording for syndrome, intractability, and absence of status epilepticus.