ICD-10 Code E83.823 – ABCC6 deficiency causing generalized arterial calcification of infancy (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code E83.823 – ABCC6 deficiency causing generalized arterial calcification of infancy
What it is
E83.823 identifies ABCC6 deficiency causing generalized arterial calcification of infancy, a rare inherited disorder that leads to abnormal calcium buildup in arteries. Use it when the diagnosis is documented as this specific genetic condition.
Clinical signs
Clinical features vary; refer to documentation. Standard references describe arterial calcification in infancy, which may present with vascular stiffness, heart failure, or ischemic complications related to narrowed or hardened arteries.
When to use this code
Use this code when the provider documents ABCC6 deficiency as the cause of generalized arterial calcification of infancy. It may also apply when the record confirms the inherited disorder and links it to the arterial calcification diagnosis. Check documentation if the cause is not clearly stated.
Do not use for
Do not use this code for nonspecific vascular calcification, age-related calcification, or other genetic disorders without ABCC6 deficiency. If the chart does not confirm the exact condition, check documentation.
Coding tip
Code only when the medical record explicitly ties ABCC6 deficiency to generalized arterial calcification of infancy.