ICD-10 Code E83.110 – Hereditary hemochromatosis (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code E83.110 – Hereditary hemochromatosis
What it is
Hereditary hemochromatosis is an inherited disorder that causes the body to absorb and store too much iron. Over time, excess iron can accumulate in organs and damage them.
Clinical signs
Clinical features vary; refer to documentation. Common findings may include fatigue, joint pain, liver enlargement, skin darkening, diabetes, or abnormal iron studies supporting iron overload.
When to use this code
Use E83.110 when the provider documents hereditary hemochromatosis, including confirmed genetic or familial iron overload. You may also use it when the assessment clearly identifies this inherited condition as the reason for evaluation or ongoing management.
Do not assign it for nonspecific iron overload without a hereditary diagnosis. Check documentation if the record only mentions elevated iron, ferritin, or suspected hemochromatosis.
Do not use for
Do not use this code for secondary hemochromatosis, transfusion-related iron overload, or unspecified iron metabolism disorders. If the chart does not clearly state hereditary disease, check documentation.
Coding tip
Code hereditary hemochromatosis only when the record supports an inherited form of iron overload, not merely abnormal iron testing.