ICD-10 Code E76.219 – Morquio mucopolysaccharidoses, unspecified (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code E76.219 – Morquio mucopolysaccharidoses, unspecified
What it is
E76.219 identifies Morquio mucopolysaccharidosis when the record does not specify a more exact type. Use it for this inherited lysosomal storage disorder when documentation only states “Morquio” or “Morquio syndrome.”
Clinical signs
Clinical features vary; refer to documentation. Commonly reported findings include skeletal dysplasia, short stature, joint laxity, and abnormal bone development, but you should code only what the provider documents.
When to use this code
Use this code when the clinician diagnoses Morquio mucopolysaccharidosis but does not document a more specific subtype. It also fits charting that confirms the disorder without further detail. If the note names a different mucopolysaccharidosis, do not use E76.219.
Do not use for
Do not use this code for other mucopolysaccharidoses, metabolic disorders, or nonspecific skeletal abnormalities without a documented Morquio diagnosis. Check documentation if the type is unclear.
Coding tip
Assign E76.219 only when Morquio mucopolysaccharidosis is explicitly documented and no more specific code is supported.