ICD-10 Code E76.210 – Morquio A mucopolysaccharidoses (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code E76.210 – Morquio A mucopolysaccharidoses
What it is
E76.210 identifies Morquio A mucopolysaccharidosis, a rare inherited lysosomal storage disorder. It is used when documentation specifies the Morquio A subtype, also called MPS IVA.
Clinical signs
Typical findings include short stature, skeletal dysplasia, joint laxity, and abnormal spine or chest development. Clinical features vary; refer to documentation for the confirmed phenotype and subtype.
When to use this code
Use this code when the record clearly states Morquio A mucopolysaccharidosis, MPS IVA, or an equivalent documented diagnosis. You may also use it when the clinician documents the disorder as confirmed, evaluated, or managed during the encounter. Check documentation if the note only says mucopolysaccharidosis without type.
Do not use for
Do not use E76.210 for other mucopolysaccharidoses, such as Morquio B or unspecified MPS. Avoid it when the chart does not identify the A subtype. Check documentation.
Coding tip
Code the specific subtype only when the provider documents Morquio A or MPS IVA explicitly.