ICD-10 Code E76.21 – Morquio mucopolysaccharidoses (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code E76.21 – Morquio mucopolysaccharidoses
What it is
E76.21 identifies Morquio mucopolysaccharidosis, a rare inherited lysosomal storage disorder. It is used when documentation specifies Morquio syndrome or mucopolysaccharidosis type IV.
Clinical signs
Clinical features vary; refer to documentation. Common findings include skeletal dysplasia, short stature, joint laxity, and abnormal bone development, with possible corneal clouding or airway and cardiac involvement.
When to use this code
Use this code when the provider documents Morquio syndrome, mucopolysaccharidosis type IV, or Morquio mucopolysaccharidosis. You may also use it when the record clearly supports this diagnosis in a confirmed genetic or metabolic workup. If the chart only says suspected storage disorder, check documentation.
Do not use for
Do not use E76.21 for other mucopolysaccharidoses, such as Hurler or Hunter syndromes. Do not assign it when the record names only skeletal dysplasia without confirming Morquio disease.
Coding tip
Confirm the exact mucopolysaccharidosis type in the assessment or problem list before assigning E76.21.