ICD-10 Code E76.2 – Other mucopolysaccharidoses (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code E76.2 – Other mucopolysaccharidoses
What it is
E76.2 identifies mucopolysaccharidosis types not classified elsewhere. Use it for inherited lysosomal storage disorders with glycosaminoglycan accumulation when the specific subtype is not documented.
Clinical signs
Clinical features vary; refer to documentation. Typical findings may include coarse facial features, skeletal abnormalities, developmental delay, organ enlargement, and progressive functional decline.
When to use this code
Assign this code when the clinician documents an “other” mucopolysaccharidosis or a specific MPS type not covered by a more precise code. It is also appropriate when the subtype is known to be a mucopolysaccharidosis, but the exact type is not stated. Do not guess the subtype from partial details.
Do not use for
Do not use E76.2 for mucopolysaccharidoses with a more specific ICD-10-CM code, such as a named subtype documented elsewhere. Check documentation if the record only says “storage disorder” without confirming mucopolysaccharidosis.
Coding tip
Query for the exact MPS subtype whenever possible; use E76.2 only when the documentation supports an unspecified or other mucopolysaccharidosis.