ICD-10 Code E71.40 – Disorder of carnitine metabolism, unspecified (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code E71.40 – Disorder of carnitine metabolism, unspecified
What it is
E71.40 identifies a disorder affecting how the body handles carnitine, a substance needed for normal energy metabolism. Use this code when the record states a carnitine metabolism disorder but does not specify the exact type.
Clinical signs
Clinical features vary; refer to documentation. Records may note abnormal carnitine handling, suspected metabolic disease, or an unspecified inherited or acquired carnitine disorder.
When to use this code
Use E71.40 when the clinician documents disorder of carnitine metabolism without naming a more specific diagnosis. It also fits when the chart confirms a carnitine-related metabolic disorder but the subtype is not available in the record. Check documentation if the condition is described only as low carnitine or a nutritional issue.
Do not use for
Do not use this code for a clearly identified, more specific carnitine disorder. It is also not appropriate when the documentation only supports a deficiency, dietary problem, or another metabolic condition. Check documentation.
Coding tip
Query for the exact carnitine disorder whenever possible, because unspecified coding should be used only when the record lacks detail.