ICD-10 Code E70.311 – Autosomal recessive ocular albinism (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code E70.311 – Autosomal recessive ocular albinism
What it is
Autosomal recessive ocular albinism is an inherited condition that mainly affects the eyes, causing reduced pigment in ocular tissues. It is coded when documentation identifies this specific genetic form of ocular albinism.
Clinical signs
Typical findings include decreased visual acuity, nystagmus, photophobia, and reduced iris or retinal pigment. Clinical features vary; refer to documentation.
When to use this code
Use this code when the provider documents autosomal recessive ocular albinism or confirms this diagnosis in the assessment. It may also apply when the record clearly links the patient’s eye findings to this inherited disorder. Do not infer the diagnosis from vision problems alone.
Do not use for
Do not use this code for nonspecific visual impairment, generalized albinism, or pigment changes without a confirmed autosomal recessive ocular albinism diagnosis. Check documentation.
Coding tip
Verify the inheritance pattern and exact diagnosis wording in the note before assigning E70.311.