ICD-10 Code E34.01 – Carcinoid Heart Syndrome (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code E34.01 – Carcinoid heart syndrome
What it is
E34.01 identifies carcinoid heart syndrome, a cardiac complication of carcinoid tumor–related hormone exposure. It reflects heart involvement, usually affecting the right-sided valves and chambers.
Clinical signs
Clinical features vary; refer to documentation. Common findings include signs of right-sided heart disease, such as tricuspid or pulmonic valve dysfunction, edema, and other evidence of carcinoid-related cardiac involvement.
When to use this code
Use this code when the provider documents carcinoid heart syndrome, carcinoid cardiopathy, or heart disease attributed to carcinoid syndrome. It is appropriate when the cardiac condition is the focus of evaluation or is clearly linked in the record. Check documentation if the note only mentions carcinoid syndrome without cardiac involvement.
Do not use for
Do not use it for carcinoid syndrome alone without heart involvement. Do not assign it when cardiac findings are unrelated to carcinoid disease or are not documented as such.
Coding tip
Code E34.01 only when the chart clearly ties the heart condition to carcinoid disease.