ICD-10 Code A50.4 – Late congenital neurosyphilis [juvenile neurosyphilis] (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code A50.4 – Late congenital neurosyphilis [juvenile neurosyphilis]
What it is
This code identifies late neurologic disease caused by congenital syphilis, typically appearing after infancy. It reflects syphilis-related damage to the nervous system in a child or adolescent.
Clinical signs
Clinical features vary; refer to documentation. Findings may include neurologic deficits, hearing or vision problems, developmental delay, seizures, or other late sequelae of congenital infection.
When to use this code
Use A50.4 when the record clearly states late congenital neurosyphilis or juvenile neurosyphilis. Apply it for documented neurologic manifestations linked to congenital syphilis in a patient beyond the newborn period. Check documentation if the note only says congenital syphilis without nervous system involvement.
Do not use for
Do not use this code for acquired syphilis, early congenital syphilis, or nonspecific neurologic symptoms without a documented congenital syphilis cause. Check documentation when the stage is unclear.
Coding tip
Code the congenital syphilis stage and the documented neurologic complication exactly as stated in the record.