ICD-10 Code E03.0 – Congenital hypothyroidism with diffuse goiter (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code E03.0 – Congenital hypothyroidism with diffuse goiter
What it is
E03.0 identifies congenital hypothyroidism present at birth with diffuse enlargement of the thyroid gland. Use it when documentation shows both congenital thyroid hormone deficiency and a diffuse goiter.
Clinical signs
Clinical features vary; refer to documentation. Common findings may include an enlarged thyroid, poor feeding, constipation, prolonged jaundice, lethargy, and delayed growth or development.
When to use this code
Use E03.0 when the record clearly states congenital hypothyroidism and diffuse goiter together. It is appropriate for newborns or children with confirmed congenital thyroid dysfunction and generalized thyroid enlargement.
If the chart mentions hypothyroidism without goiter, or goiter without congenital hypothyroidism, choose a different code. Check documentation when the thyroid description is nonspecific or incomplete.
Do not use for
Do not use this code for acquired hypothyroidism, nodular goiter, or unspecified thyroid enlargement. If the condition is not documented as congenital, this code is not appropriate.
Coding tip
Confirm both congenital hypothyroidism and diffuse goiter are documented before assigning E03.0.