ICD-10 Code E00.2 – Congenital iodine-deficiency syndrome, mixed type (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code E00.2 – Congenital iodine-deficiency syndrome, mixed type
What it is
E00.2 identifies congenital iodine-deficiency syndrome, mixed type. Use it for a congenital condition caused by iodine deficiency that shows more than one classic feature pattern.
Clinical signs
Clinical features vary; refer to documentation. Common findings may include congenital hypothyroidism with growth delay, developmental impairment, and physical changes consistent with iodine deficiency.
When to use this code
Use this code when the provider documents congenital iodine-deficiency syndrome, mixed type, or an equivalent diagnosis. It is appropriate when the record supports a congenital iodine-deficiency disorder with mixed manifestations rather than a single subtype. Check documentation if the type is not clearly stated.
Do not use for
Do not use it for acquired hypothyroidism, simple iodine deficiency without congenital syndrome, or unspecified congenital thyroid disorders. If the chart does not clearly support the mixed type, check documentation.
Coding tip
Assign E00.2 only when the congenital mixed type is explicitly documented; otherwise, query the provider.