ICD-10 Code E00.0 – Congenital iodine-deficiency syndrome, neurological type (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code E00.0 – Congenital iodine-deficiency syndrome, neurological type
What it is
E00.0 identifies a congenital iodine-deficiency syndrome with neurological involvement. Use it for infants or children whose condition is documented as the neurological type of congenital iodine deficiency.
Clinical signs
Clinical features vary; refer to documentation. Standard references describe neurodevelopmental impairment, intellectual disability, speech or motor delay, and other neurologic findings linked to congenital iodine deficiency.
When to use this code
Use this code when the provider documents congenital iodine-deficiency syndrome, neurological type, or clearly states congenital iodine deficiency with neurologic manifestations. It fits confirmed congenital cases, not suspected exposure alone. If the record only says iodine deficiency without the congenital neurologic type, check documentation.
Do not use for
Do not use E00.0 for acquired iodine deficiency, isolated hypothyroidism, or nonspecific developmental delay without documentation of congenital iodine-deficiency syndrome. If the chart does not specify the neurological type, check documentation.
Coding tip
Code from the provider’s exact wording; the congenital and neurologic elements both matter.