ICD-10 Code D75.0 – Familial erythrocytosis (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code D75.0 – Familial erythrocytosis
What it is
D75.0 identifies familial erythrocytosis, an inherited condition marked by increased red blood cell production. Use it when the record documents a family-linked erythrocytosis rather than an acquired cause.
Clinical signs
Clinical features vary; refer to documentation. Commonly noted findings include persistent erythrocytosis, possible family history, and symptoms related to increased blood viscosity or reduced oxygen delivery.
When to use this code
Use D75.0 when the clinician documents familial, hereditary, or congenital erythrocytosis. It also fits cases where the chart clearly distinguishes the condition from secondary erythrocytosis or polycythemia vera. If the cause is not specified, check documentation before coding.
Do not use for
Do not use this code for acquired erythrocytosis from hypoxia, smoking, tumors, or medications. It is also not the right choice for polycythemia vera.
Coding tip
Confirm that the record explicitly links erythrocytosis to a familial or inherited cause before assigning D75.0.