ICD-10 Code I01.8 – Other acute rheumatic heart disease (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code I01.8 – Other acute rheumatic heart disease
What it is
I01.8 identifies acute rheumatic heart disease that does not fit a more specific rheumatic carditis category. It reflects active rheumatic involvement of the heart, usually after streptococcal infection.
Clinical signs
Clinical features vary; refer to documentation. You may see evidence of carditis, new or changing murmurs, heart enlargement, or heart failure symptoms in the setting of acute rheumatic fever.
When to use this code
Use this code when the record clearly documents other acute rheumatic heart disease and does not name a more specific acute rheumatic cardiac diagnosis. It is appropriate for active rheumatic heart involvement, not remote or healed disease. Check documentation for the exact cardiac manifestation and whether acute rheumatic fever is also reported.
Do not use for
Do not use this code for chronic rheumatic heart disease or for rheumatic heart disease with a more specific code available. If the chart only says “heart murmur” or “history of rheumatic fever,” check documentation.
Coding tip
Confirm the record links the cardiac finding to an acute rheumatic process before assigning I01.8.