ICD-10 Code I01.2 – Acute rheumatic myocarditis (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code I01.2 – Acute rheumatic myocarditis
What it is
Use this code for myocarditis occurring as part of acute rheumatic fever. It reflects inflammatory heart muscle involvement linked to a recent streptococcal infection.
Clinical signs
Clinical features vary; refer to documentation. Commonly, you may see evidence of acute rheumatic fever with cardiac involvement, such as new murmur, tachycardia, or signs of heart failure.
When to use this code
Assign I01.2 when the record specifically states acute rheumatic myocarditis or rheumatic heart inflammation affecting the myocardium. Use it with documented acute rheumatic fever, not with nonspecific myocarditis alone. Check documentation for the exact rheumatic manifestation.
Do not use for
Do not use this code for myocarditis without a rheumatic cause, or for chronic rheumatic heart disease. If the provider does not link the myocarditis to acute rheumatic fever, check documentation.
Coding tip
Always confirm that the provider documents an acute rheumatic etiology before choosing I01.2.