ICD-10 Code I01.1 – Acute rheumatic endocarditis (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code I01.1 – Acute rheumatic endocarditis
What it is
I01.1 identifies acute inflammation of the endocardium linked to rheumatic fever. You use it when the record documents rheumatic heart involvement affecting the valve lining or heart chambers.
Clinical signs
Clinical features vary; refer to documentation. Typical findings may include new or changing heart murmurs, evidence of valvular inflammation, and other signs of active rheumatic carditis.
When to use this code
Use this code when the provider clearly documents acute rheumatic endocarditis or acute rheumatic carditis with endocardial involvement. It may appear in cases of active rheumatic fever affecting the heart. Code only when the diagnosis is established in the chart.
Do not use for
Do not use this code for nonrheumatic endocarditis, chronic rheumatic valve disease, or a history of rheumatic fever without current acute endocardial involvement. Check documentation if the term is vague.
Coding tip
Confirm that “acute” and “rheumatic” are both documented before assigning I01.1.