ICD-10 Code E71.111 – 3-methylglutaconic aciduria (2026): Diagnosis, Symptoms & Billing Guide
The ICD-10 code for 3-methylglutaconic aciduria is E71.111.2026 ICD-10-CM Diagnosis Code E71.111 – 3-methylglutaconic aciduria Related ICD-10 Codes Parent code: E71 – Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism Other codes in same category: E71.0 – Maple-syrup-urine disease, E71.1 – Other disorders of branched-chain amino-acid metabolism, E71.11 – Branched-chain organic acidurias, E71.110 – Isovaleric…