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      ICD-10 Code E71.111 – 3-methylglutaconic aciduria (2026): Diagnosis, Symptoms & Billing Guide

      ByAdmin May 16, 2026

      The ICD-10 code for 3-methylglutaconic aciduria is E71.111.2026 ICD-10-CM Diagnosis Code E71.111 – 3-methylglutaconic aciduria Related ICD-10 Codes Parent code: E71 – Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism Other codes in same category: E71.0 – Maple-syrup-urine disease, E71.1 – Other disorders of branched-chain amino-acid metabolism, E71.11 – Branched-chain organic acidurias, E71.110 – Isovaleric…

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    • Codes

      ICD-10 Code E71.110 – Isovaleric acidemia (2026): Diagnosis, Symptoms & Billing Guide

      ByAdmin May 16, 2026

      The ICD-10 code for Isovaleric acidemia is E71.110.2026 ICD-10-CM Diagnosis Code E71.110 – Isovaleric acidemia Related ICD-10 Codes Parent code: E71 – Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism Other codes in same category: E71.0 – Maple-syrup-urine disease, E71.1 – Other disorders of branched-chain amino-acid metabolism, E71.11 – Branched-chain organic acidurias, E71.111 – 3-methylglutaconic…

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    • Codes

      ICD-10 Code E71.11 – Branched-chain organic acidurias (2026): Diagnosis, Symptoms & Billing Guide

      ByAdmin May 16, 2026

      The ICD-10 code for Branched-chain organic acidurias is E71.11.2026 ICD-10-CM Diagnosis Code E71.11 – Branched-chain organic acidurias Related ICD-10 Codes Parent code: E71 – Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism Other codes in same category: E71.0 – Maple-syrup-urine disease, E71.1 – Other disorders of branched-chain amino-acid metabolism, E71.110 – Isovaleric acidemia, E71.111 –…

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    • Codes

      ICD-10 Code E71.1 – Other disorders of branched-chain amino-acid metabolism (2026): Diagnosis, Symptoms & Billing Guide

      ByAdmin May 16, 2026

      The ICD-10 code for Other disorders of branched-chain amino-acid metabolism is E71.1.2026 ICD-10-CM Diagnosis Code E71.1 – Other disorders of branched-chain amino-acid metabolism Related ICD-10 Codes Parent code: E71 – Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism Other codes in same category: E71.0 – Maple-syrup-urine disease, E71.11 – Branched-chain organic acidurias, E71.110 – Isovaleric…

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    • Codes

      ICD-10 Code E71.0 – Maple-syrup-urine disease (2026): Diagnosis, Symptoms & Billing Guide

      ByAdmin May 16, 2026

      The ICD-10 code for Maple-syrup-urine disease is E71.0.2026 ICD-10-CM Diagnosis Code E71.0 – Maple-syrup-urine disease Related ICD-10 Codes Parent code: E71 – Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism Other codes in same category: E71.1 – Other disorders of branched-chain amino-acid metabolism, E71.11 – Branched-chain organic acidurias, E71.110 – Isovaleric acidemia, E71.111 – 3-methylglutaconic…

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    • Codes

      ICD-10 Code E71 – Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism (2026): Diagnosis, Symptoms & Billing Guide

      ByAdmin May 16, 2026

      The ICD-10 code for Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism is E71.2026 ICD-10-CM Diagnosis Code E71 – Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism Related ICD-10 Codes More specific subcodes: E71.0 – Maple-syrup-urine disease, E71.1 – Other disorders of branched-chain amino-acid metabolism, E71.11 – Branched-chain organic acidurias, E71.110 – Isovaleric acidemia, E71.111…

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    • Codes

      ICD-10 Code E70.9 – Disorder of aromatic amino-acid metabolism, unspecified (2026): Diagnosis, Symptoms & Billing Guide

      ByAdmin May 16, 2026

      The ICD-10 code for Disorder of aromatic amino-acid metabolism, unspecified is E70.9.2026 ICD-10-CM Diagnosis Code E70.9 – Disorder of aromatic amino-acid metabolism, unspecified Related ICD-10 Codes Parent code: E70 – Disorders of aromatic amino-acid metabolism Other codes in same category: E70.0 – Classical phenylketonuria, E70.1 – Other hyperphenylalaninemias, E70.2 – Disorders of tyrosine metabolism, E70.20…

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    • Codes

      ICD-10 Code E70.89 – Other disorders of aromatic amino-acid metabolism (2026): Diagnosis, Symptoms & Billing Guide

      ByAdmin May 16, 2026

      The ICD-10 code for Other disorders of aromatic amino-acid metabolism is E70.89.2026 ICD-10-CM Diagnosis Code E70.89 – Other disorders of aromatic amino-acid metabolism Related ICD-10 Codes Parent code: E70 – Disorders of aromatic amino-acid metabolism Other codes in same category: E70.0 – Classical phenylketonuria, E70.1 – Other hyperphenylalaninemias, E70.2 – Disorders of tyrosine metabolism, E70.20…

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    • Codes

      ICD-10 Code E70.81 – Aromatic L-amino acid decarboxylase deficiency (2026): Diagnosis, Symptoms & Billing Guide

      ByAdmin May 16, 2026

      The ICD-10 code for Aromatic L-amino acid decarboxylase deficiency is E70.81.2026 ICD-10-CM Diagnosis Code E70.81 – Aromatic L-amino acid decarboxylase deficiency Related ICD-10 Codes Parent code: E70 – Disorders of aromatic amino-acid metabolism Other codes in same category: E70.0 – Classical phenylketonuria, E70.1 – Other hyperphenylalaninemias, E70.2 – Disorders of tyrosine metabolism, E70.20 – Disorder…

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    • Codes

      ICD-10 Code E70.8 – Other disorders of aromatic amino-acid metabolism (2026): Diagnosis, Symptoms & Billing Guide

      ByAdmin May 16, 2026

      The ICD-10 code for Other disorders of aromatic amino-acid metabolism is E70.8.2026 ICD-10-CM Diagnosis Code E70.8 – Other disorders of aromatic amino-acid metabolism Related ICD-10 Codes Parent code: E70 – Disorders of aromatic amino-acid metabolism Other codes in same category: E70.0 – Classical phenylketonuria, E70.1 – Other hyperphenylalaninemias, E70.2 – Disorders of tyrosine metabolism, E70.20…

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