ICD-10 Code E78.010 – Homozygous familial hypercholesterolemia [HoFH] (2026): Diagnosis, Symptoms & Billing Guide
The ICD-10 code for Homozygous familial hypercholesterolemia [HoFH] is E78.010.2026 ICD-10-CM Diagnosis Code E78.010 – Homozygous familial hypercholesterolemia [HoFH] Related ICD-10 Codes Parent code: E78 – Disorders of lipoprotein metabolism and other lipidemias Other codes in same category: E78.0 – Pure hypercholesterolemia, E78.00 – Pure hypercholesterolemia, unspecified, E78.01 – Familial hypercholesterolemia, E78.011 – Heterozygous familial…