ICD-10 Code H47.22 – Hereditary optic atrophy (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code H47.22 – Hereditary optic atrophy
What it is
Hereditary optic atrophy is an inherited disorder that causes gradual damage to the optic nerve. It leads to progressive vision loss, often beginning in childhood or early adulthood.
Clinical signs
Typical findings include decreased visual acuity, color vision impairment, and optic disc pallor. Visual field defects may be present; clinical features vary, so refer to documentation.
When to use this code
Use H47.22 when the record documents hereditary optic atrophy or a clearly inherited optic nerve atrophy. Apply it for confirmed familial cases with progressive optic nerve degeneration. If the note only says optic atrophy without hereditary cause, check documentation before coding.
Do not use for
Do not use this code for optic atrophy from trauma, inflammation, ischemia, or other acquired causes. If hereditary etiology is not documented, choose a more specific documented diagnosis or check documentation.
Coding tip
Look for wording such as “hereditary,” “familial,” or a named inherited optic neuropathy before assigning H47.22.