ICD-10 Code H47.03 – Optic nerve hypoplasia (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code H47.03 – Optic nerve hypoplasia
What it is
Optic nerve hypoplasia is an underdevelopment of the optic nerve, usually present from birth. It can affect one or both eyes and may reduce visual function.
Clinical signs
Common findings include reduced visual acuity, nystagmus, strabismus, and a small optic disc on eye examination. Clinical features vary; refer to documentation.
When to use this code
Use H47.03 when the provider documents optic nerve hypoplasia as the confirmed diagnosis. It fits congenital or longstanding optic nerve underdevelopment noted on ophthalmic exam or imaging. Code the condition when it is the reason for the visit or a documented active diagnosis.
Do not use for
Do not use this code for optic neuritis, optic atrophy, or nonspecific vision loss without documented hypoplasia. Check documentation if the record only describes abnormal optic disc appearance.
Coding tip
Assign the code only when hypoplasia is explicitly documented; if laterality is unclear, follow the record and query if needed.