ICD-10 Code H18.593 – Other hereditary corneal dystrophies, bilateral (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code H18.593 – Other hereditary corneal dystrophies, bilateral
What it is
This code identifies a bilateral, inherited corneal dystrophy that does not fit a more specific named category. It means both corneas are affected by a hereditary, usually noninflammatory, structural disorder.
Clinical signs
Findings may include bilateral corneal opacities, deposits, or progressive visual blur. Clinical features vary; refer to documentation for the specific dystrophy pattern and severity.
When to use this code
Use H18.593 when the provider documents a hereditary corneal dystrophy in both eyes and no more specific corneal dystrophy code applies. It is appropriate when the record confirms bilateral involvement and the condition is not better described by another hereditary corneal dystrophy diagnosis. Check documentation if the subtype is unclear.
Do not use for
Do not use this code for unilateral corneal dystrophy or for corneal disease caused by infection, trauma, or inflammation. If the chart names a specific hereditary corneal dystrophy, code that specific condition instead.
Coding tip
Confirm both heredity and bilateral involvement in the provider note before assigning H18.593.