ICD-10 Code H18.591 – Other hereditary corneal dystrophies, right eye (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code H18.591 – Other hereditary corneal dystrophies, right eye
What it is
This code identifies a hereditary dystrophy affecting the cornea in the right eye that does not fit a more specific corneal dystrophy category. Use it when the documentation names a genetic corneal dystrophy limited to the right eye.
Clinical signs
Clinical features vary; refer to documentation. Findings may include corneal opacity, recurrent visual disturbance, or characteristic corneal changes noted on examination, but the exact pattern depends on the specific dystrophy.
When to use this code
Use H18.591 when the provider documents an inherited corneal dystrophy affecting only the right eye and does not name a more specific ICD-10 option. It is appropriate for ophthalmology notes, problem lists, or claims tied to a confirmed hereditary corneal disorder. If laterality is not documented, check documentation before coding.
Do not use for
Do not use this code for nonhereditary corneal disease, corneal scarring from injury, or bilateral disease coded elsewhere. If the diagnosis is more specific, or the eye laterality is different, choose the documented code instead.
Coding tip
Confirm both heredity and right-eye laterality in the record before assigning H18.591.