ICD-10 Code H18.55 – Macular corneal dystrophy (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code H18.55 – Macular corneal dystrophy
What it is
H18.55 identifies macular corneal dystrophy, a hereditary disorder that causes progressive clouding of the cornea. It affects the corneal stroma and can reduce vision over time.
Clinical signs
Typical findings include bilateral corneal opacities and gradual visual impairment. Clinical features vary; refer to documentation if the record does not clearly describe the dystrophy.
When to use this code
Use H18.55 when the provider documents macular corneal dystrophy by name or clearly describes this inherited corneal dystrophy. It is appropriate for ophthalmology visits, problem lists, and confirmed diagnoses affecting vision. Check documentation if the note only mentions corneal haze or opacity without specificity.
Do not use for
Do not use this code for other corneal dystrophies, nonspecific corneal opacity, or corneal scarring from injury or infection. If the diagnosis is uncertain, check documentation.
Coding tip
Code only when the record supports macular corneal dystrophy specifically; vague corneal clouding needs clarification.