ICD-10 Code G90.0 – Idiopathic peripheral autonomic neuropathy (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code G90.0 – Idiopathic peripheral autonomic neuropathy
What it is
This code identifies a peripheral autonomic neuropathy with no known cause. It refers to dysfunction of the autonomic nerves that control involuntary body functions.
Clinical signs
Clinical features vary; refer to documentation. Typical findings may include abnormal sweating, blood pressure instability, or other autonomic symptoms affecting the limbs or peripheral nerves.
When to use this code
Use G90.0 when the provider documents idiopathic peripheral autonomic neuropathy or an equivalent diagnosis and no underlying cause is identified. Code it when the record describes autonomic nerve dysfunction without a secondary explanation. If the cause is stated, check documentation for a more specific code.
Do not use for
Do not use this code for autonomic neuropathy due to diabetes, amyloidosis, drugs, or another documented condition. Also avoid it when the chart only says peripheral neuropathy without autonomic involvement.
Coding tip
Verify that “idiopathic” and “autonomic” are both documented before assigning G90.0.