ICD-10 Code G71.29 – Other congenital myopathy (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code G71.29 – Other congenital myopathy
What it is
Use this code for a congenital muscle disorder present from birth or early life that does not fit a more specific myopathy category. It covers other inherited or developmental myopathies documented by the provider.
Clinical signs
Clinical features vary; refer to documentation. Common findings may include hypotonia, muscle weakness, delayed motor milestones, or reduced muscle tone, but the exact pattern depends on the specific congenital myopathy.
When to use this code
Assign G71.29 when the provider documents a congenital myopathy and no more specific ICD-10-CM code is available. Use it for confirmed cases described as “other congenital myopathy,” “unspecified congenital myopathy,” or a named condition not indexed elsewhere.
Check the record for the underlying diagnosis, genetic findings, and whether the condition is congenital versus acquired. If the documentation identifies a more specific myopathy type, code that diagnosis instead.
Do not use for
Do not use this code for acquired muscle disease, inflammatory myopathy, or neuromuscular disorders that are not congenital. If the chart gives a more specific congenital myopathy code, use that code instead.
Coding tip
Code only when the provider clearly documents a congenital myopathy; otherwise, check documentation and query for specificity.