ICD-10 Code G71.228 – Other centronuclear myopathy (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code G71.228 – Other centronuclear myopathy
What it is
G71.228 identifies centronuclear myopathy that does not fit a more specific subtype. It is a rare inherited muscle disorder in which muscle fibers show centrally placed nuclei and weakness is usually longstanding.
Clinical signs
Typical findings include hypotonia, delayed motor milestones, proximal muscle weakness, and reduced muscle tone. Clinical features vary; refer to documentation for the exact phenotype, genetic result, or biopsy findings.
When to use this code
Use this code when the provider documents other centronuclear myopathy without naming a more specific genetic or pathologic subtype. It also fits cases described by biopsy or genetic testing when the record clearly supports centronuclear myopathy but not a narrower diagnosis.
If the note says “centronuclear myopathy” with no further detail, confirm whether the clinician intends this unspecified other category. Check documentation when the chart mentions related congenital myopathy terms or overlapping neuromuscular disorders.
Do not use for
Do not use it for a more specific centronuclear myopathy subtype or for another muscular dystrophy, congenital myopathy, or motor neuron disorder. If the diagnosis is unclear, check documentation before coding.
Coding tip
Code the most specific myopathy documented, and query for subtype details when the record only says centronuclear myopathy.