ICD-10 Code G71.11 – Myotonic Muscular Dystrophy (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code G71.11 – Myotonic muscular dystrophy
What it is
G71.11 identifies myotonic muscular dystrophy, an inherited muscle disorder that causes progressive weakness and delayed relaxation after contraction. Use it when the record documents this specific diagnosis.
Clinical signs
Common findings include myotonia, distal muscle weakness, and muscle wasting. Patients may also have facial weakness, cataracts, or cardiac conduction abnormalities; clinical features vary, so refer to documentation.
When to use this code
Use G71.11 when the provider documents myotonic muscular dystrophy, including confirmed type 1 or type 2 if the record does not specify a different code. It is appropriate for outpatient visits, inpatient stays, and problem-list coding when the condition is active or relevant to care.
Do not use for
Do not use this code for other muscular dystrophies, nonspecific muscle weakness, or myotonia without a documented dystrophy diagnosis. Check documentation if the chart only says “muscular dystrophy.”
Coding tip
Code the condition only when the provider clearly names myotonic muscular dystrophy; if subtype details are present, capture them exactly as documented.