ICD-10 Code G40.C0 – Lafora progressive myoclonus epilepsy, not intractable (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code G40.C0 – Lafora progressive myoclonus epilepsy, not intractable
What it is
G40.C0 identifies Lafora progressive myoclonus epilepsy that is not described as intractable. It is a specific epilepsy diagnosis used when the chart documents Lafora disease with progressive myoclonic seizures.
Clinical signs
Typical findings include progressive myoclonus, generalized seizures, and neurologic decline consistent with Lafora disease. Clinical features vary; refer to documentation.
When to use this code
Use this code when the provider documents Lafora progressive myoclonus epilepsy and does not state that it is intractable or drug resistant. It may also apply when the record clearly identifies Lafora disease with epilepsy and seizure progression. If the wording is unclear, check documentation.
Do not use for
Do not use it for other epilepsy types, isolated myoclonus, or generalized seizure disorders without Lafora disease. Do not assign it when the record specifies intractable epilepsy instead.
Coding tip
Match the code to the exact provider wording and verify whether “not intractable” is documented.