ICD-10 Code G40.311 – Generalized idiopathic epilepsy and epileptic syndromes, intractable, with status epilepticus (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code G40.311 – Generalized idiopathic epilepsy and epileptic syndromes, intractable, with status epilepticus
What it is
This code identifies a generalized idiopathic epilepsy syndrome that is not controlled by treatment and is currently in status epilepticus. It applies when seizures are part of a recognized generalized epilepsy pattern and persist or recur without recovery.
Clinical signs
Clinical features vary; refer to documentation. You may see generalized seizure activity, impaired awareness, and prolonged or repeated seizures consistent with status epilepticus, along with an established diagnosis of idiopathic generalized epilepsy.
When to use this code
Use this code when the provider documents generalized idiopathic epilepsy or an idiopathic generalized epilepsy syndrome that is intractable and accompanied by status epilepticus. The record should support both the epilepsy type and the refractory nature of the condition. If status epilepticus is not documented, do not assume it.
Do not use for
Do not use this code for controlled epilepsy, a single isolated seizure, or status epilepticus without documentation of generalized idiopathic epilepsy. Check documentation if the seizure type, control status, or syndrome classification is unclear.
Coding tip
Confirm all three elements in the record: generalized idiopathic epilepsy, intractable, and status epilepticus.