ICD-10 Code E75.19 – Other gangliosidosis (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code E75.19 – Other gangliosidosis
What it is
Use this code for gangliosidosis not described by a more specific ICD-10-CM code. It identifies an inherited lysosomal storage disorder involving abnormal accumulation of gangliosides.
Clinical signs
Clinical features vary; refer to documentation. Common findings may include progressive neurologic decline, developmental delay or regression, hypotonia, and organ involvement consistent with a storage disorder.
When to use this code
Use E75.19 when the provider documents other gangliosidosis, gangliosidosis NOS, or a gangliosidosis diagnosis that does not fit a more specific code. You may also use it when the record confirms the disorder but does not name the subtype. Check documentation for the exact condition.
Do not use for
Do not use this code if the record identifies a specific gangliosidosis subtype with its own ICD-10-CM code. Do not use it for unrelated metabolic or neurologic disorders without documentation of gangliosidosis.
Coding tip
Look for the exact subtype in the assessment, genetic report, or problem list before defaulting to E75.19.