ICD-10 Code L94.1 – Linear scleroderma (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code L94.1 – Linear scleroderma
What it is
L94.1 identifies linear scleroderma, a localized scleroderma pattern that causes a line-shaped area of skin thickening and hardening. It usually affects one body region and is not the same as systemic sclerosis.
Clinical signs
Typical findings include a linear, indurated, shiny plaque that may be pigmented, atrophic, or bound down to deeper tissue. Clinical features vary; refer to documentation.
When to use this code
Use L94.1 when the provider documents linear scleroderma, including localized “en coup de sabre” or limb involvement if stated. Code it from the confirmed diagnosis, not from a nonspecific rash or skin tightening alone. Check documentation if the record does not clearly identify the subtype.
Do not use for
Do not use this code for systemic sclerosis, morphea without linear pattern, or other unspecified connective tissue disorders. If the note only says “scleroderma” without type, check documentation.
Coding tip
Capture the exact subtype and location from the clinician’s note, because “linear” distinguishes this code from other localized scleroderma forms.