ICD-10 Code K00.5 – Hereditary disturbances in tooth structure, not elsewhere classified (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code K00.5 – Hereditary disturbances in tooth structure, not elsewhere classified
What it is
K00.5 identifies inherited abnormalities affecting tooth structure, such as enamel or dentin defects, that are not classified elsewhere. Use it when the chart describes a hereditary developmental problem of the teeth.
Clinical signs
Findings may include discolored, fragile, pitted, or unusually shaped teeth. Clinical features vary; refer to documentation, and confirm the hereditary nature when it is stated in the record.
When to use this code
Use K00.5 when the provider documents a hereditary defect in tooth structure and does not assign a more specific diagnosis. It fits congenital or familial enamel or dentin disorders described in the assessment. If the note only says “tooth abnormality,” check documentation before coding.
Do not use for
Do not use this code for acquired tooth damage from trauma, decay, or wear. It is also not the best choice when the record identifies a different specific developmental tooth disorder.
Coding tip
Look for wording such as “hereditary,” “familial,” or a named enamel/dentin defect before assigning K00.5.