ICD-10 Code I27.840 – Fontan-associated liver disease [FALD] (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code I27.840 – Fontan-associated liver disease [FALD]
What it is
Fontan-associated liver disease refers to liver injury that develops after a Fontan circulation. Use this code for documented hepatic disease linked to the Fontan procedure and its long-term circulatory effects.
Clinical signs
Clinical features vary; refer to documentation. Commonly recorded findings include chronic liver congestion, fibrosis, cirrhosis, portal hypertension, or imaging abnormalities in a patient with prior Fontan surgery.
When to use this code
Use this code when the provider specifically documents Fontan-associated liver disease, Fontan-related hepatic fibrosis, or a similar diagnosis tied to Fontan physiology. It may also apply when the note clearly identifies liver disease as a complication of the Fontan circulation. Check documentation if the record only mentions abnormal liver tests without a linked diagnosis.
Do not use for
Do not use this code for general liver disease, hepatitis, or cirrhosis without a stated Fontan association. If the relationship to the Fontan procedure is not documented, code the condition that is actually confirmed.
Coding tip
Look for explicit wording connecting the liver condition to Fontan circulation before assigning I27.840.