ICD-10 Code I27.22 – Pulmonary hypertension due to left heart disease (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code I27.22 – Pulmonary hypertension due to left heart disease
What it is
This code identifies pulmonary hypertension that develops because of left-sided heart disease. It reflects elevated pressure in the lung circulation caused by backflow or increased filling pressure from the left heart.
Clinical signs
Clinical features vary; refer to documentation. Common findings may include exertional dyspnea, fatigue, and evidence of left heart disease such as heart failure, valvular disease, or cardiomyopathy.
When to use this code
Use I27.22 when the provider documents pulmonary hypertension specifically attributed to left heart disease. The record should link the pulmonary hypertension to the left-sided cardiac condition, not just mention both diagnoses separately.
Use it for cases where the cause is documented as left ventricular dysfunction, mitral valve disease, or another left heart disorder. Check documentation if the relationship is unclear or if another pulmonary hypertension cause is stated.
Do not use for
Do not use this code for primary pulmonary arterial hypertension or pulmonary hypertension from lung disease, thromboembolic disease, or other non-left-heart causes. Do not assign it when the chart does not establish the cause.
Coding tip
Code the underlying left heart condition as well, and verify the provider explicitly links it to the pulmonary hypertension.