ICD-10 Code I27.1 – Kyphoscoliotic heart disease (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code I27.1 – Kyphoscoliotic heart disease
What it is
I27.1 identifies pulmonary heart disease associated with kyphoscoliosis. Use it when spinal deformity contributes to chronic strain on the right side of the heart.
Clinical signs
Clinical features vary; refer to documentation. Commonly, records describe kyphoscoliosis with evidence of right heart involvement or pulmonary hypertension related to restrictive chest mechanics.
When to use this code
Use this code when the provider documents kyphoscoliotic heart disease or pulmonary heart disease caused by kyphoscoliosis. It fits cases where the spinal deformity is the stated underlying contributor to cardiac strain. If the record only mentions kyphoscoliosis without heart involvement, do not assign I27.1.
Do not use for
Do not use this code for kyphoscoliosis alone, or for other forms of pulmonary hypertension without a documented kyphoscoliotic cause. Check documentation when the relationship to heart disease is unclear.
Coding tip
Assign I27.1 only when the documentation links the heart disease to kyphoscoliosis.